Inclusion CIM-10 : Hydrops fetalis due to alpha thalassemia; Triple gene defect alpha thalassemia; Severe alpha thalassemia; Alpha thalassemia major; Hemoglobin H disease; Hemoglobin H Constant Spring;
ICD-10 exclusion note : hydrops fetalis not due to immune hemolysis (P83.2); alpha thalassemia trait or minor (D56.3); asymptomatic alpha thalassemia (D56.3); hydrops fetalis due to isoimmunization (P56.0);