ICD-11 definition : Peutz-Jeghers syndrome (PJS) is an autosomal dominant inherited disorder characterized
by intestinal hamartomatous polyps in association with a distinct pattern of skin
and mucosal macular melanin deposition. Patients have an increased risk of developing
intestinal cancer.;
Peutz-Jeghers syndrome (PJS) is an autosomal dominant inherited disorder characterized
by intestinal hamartomatous polyps in association with a distinct pattern of skin
and mucosal macular melanin deposition. Patients have an increased risk of developing
intestinal cancer.