Polycythaemia vera

ICD-11 code : 2A20.4;

Preferred Label : Polycythaemia vera;

ICD-11 definition : Polycythaemia vera (PV) is a clonal myeloproliferative neoplasm characterized by erythrocytosis frequently accompanied by leukocytosis, and/or thrombocytosis, and an associated increased risk of haemorrhagic and thrombotic (venous and arterial) complications. JAK2 p.V617F and JAK2 (Janus kinase 2) exon12 mutations have been strongly associated with PV.;

ICD-11 synonym : Vaquez disease; primary polycythaemia; Heilmeyer-Schoner disease; polycythaemia rubra vera; Vaquez Osler disease;

Details

Origin ID

818364947;

UMLS CUI

C0032463;

Automatic exact mappings (from CISMeF team)
- Benign, uncertain or in-situ neoplasm of blood, blood-forming organs and immune system [ICPC-3 diagnosis]
Currated CISMeF NLP mapping
- Polycythaemia rubra vera [MedDRA LLT]
- Polycythaemia vera [MedDRA Preferred Term]
- Polycythaemia vera [ICD-10 category (who)]
- Polycythemia Vera [NCIt concept]
- Polycythemia vera [ORDO Disease]
- Polycythemia vera (disorder) [SNOMED CT concept]
- Polycythemia vera (morphologic abnormality) [SNOMED CT concept]
- Primary polycythaemia [MedDRA LLT]
- Vaquez's disease [MedDRA LLT]
- polycythemia vera [MeSH Descriptor]
- polycythemia vera [DO Concept]
ICD-10 Mapping
- Polycythemia vera [ICD-10 category]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Polycythaemia rubra vera [MedDRA LLT]
- Polycythaemia vera [MedDRA Preferred Term]
- Polycythemia Vera [NCIt concept]
- Polycythemia rubra vera [MedDRA LLT]
- Polycythemia vera [ICD-O code]
- Polycythemia vera [ICD-9 code]
- Polycythemia vera [ICD-10 category]
- Polycythemia vera [MedDRA LLT]
- Polycythemia vera [OMIM Phenotype]
- Polycythemia vera [ORDO Disease]
- Polycythemia vera [PASCAL descriptor]
- Polycythemia vera (disorder) [SNOMED CT concept]
- Polycythemia vera (morphologic abnormality) [SNOMED CT concept]
- Primary polycythaemia [MedDRA LLT]
- Primary polycythemia [MedDRA LLT]
- Vaquez's disease [MedDRA LLT]
- polycythemia vera [DO Concept]
- polycythemia vera [MeSH Descriptor]
- polycythemia vera [MeSH concept]
- polycythemia vera [Disease (Nov.)]
- polycythemia vera [Radlex concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients