Gamma heavy chain disease

ICD-11 code : 2A84.1;

Preferred Label : Gamma heavy chain disease;

ICD-11 definition : A clonal disorder characterized by the secretion of a truncated gamma chain. In most cases, it is associated with morphologic changes also seen in lymphoplasmacytic lymphomas, but the clinical course is typically more aggressive than in lymphoplasmacytic lymphoma/Waldenstrom's macroglobulinemia.;

ICD-11 synonym : Franklin disease;

ICD-11 inclusion : Franklin disease;

Details

Origin ID

705015637;

Currated CISMeF NLP mapping
- Gamma Heavy Chain Disease [NCIt concept]
- Gamma heavy chain disease [ICD-10 Sub-category (who)]
- Gamma heavy chain disease (disorder) [SNOMED CT concept]
- Gamma-heavy chain disease [ORDO Disease]
- Heavy chain disease [ICD-10 Sub-category]
- Heavy chain disease (morphologic abnormality) [SNOMED CT concept]
- alpha heavy chain disease [SNOMED Notion]
- gamma heavy chain disease [DO Concept]
- gamma-Chain disease [MeSH concept]
- heavy chain disease [MeSH Descriptor]
- γ-Heavy chain disease [PASCAL descriptor]
ICD-10 Mapping
- Malignant immunoproliferative diseases and certain other B-cell lymphomas [ICD-10 category]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients