ICD-11 code : 8D87.0;
Preferred Label : Multiple system atrophy;
ICD-11 definition : Multiple system atrophy (MSA) is a rare neurodegenerative disorder characterized by
varied combinations of parkinsonian, cerebellar, autonomic (erectile dysfunction,
bladder dysfunction), orthostatic hypotension) and pyramidal features. The disease
belongs to the group of alpha-synucleinopathies, a group of diseases characterized
by aggregation of alpha-synuclein in affected brain regions. There are two different
types MSA-P (with parkinsonism) and MSA-C ( with cerebellar dysfunction);
ICD-11 synonym : multisystem atrophy;
ICD-11 "other" category code : 8D87.0Y;
ICD-11 "unspecified" category code : 8D87.0Z;
Origin ID : 1890931931;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Multiple system atrophy (MSA) is a rare neurodegenerative disorder characterized by
varied combinations of parkinsonian, cerebellar, autonomic (erectile dysfunction,
bladder dysfunction), orthostatic hypotension) and pyramidal features. The disease
belongs to the group of alpha-synucleinopathies, a group of diseases characterized
by aggregation of alpha-synuclein in affected brain regions. There are two different
types MSA-P (with parkinsonism) and MSA-C ( with cerebellar dysfunction)