ICD-11 definition : A chronic myeloproliferative neoplasm that involves primarily the megakaryocytic lineage.
It is characterized by sustained thrombocytosis in the blood, increased numbers of
large, mature megakaryocytes in the bone marrow, and episodes of thrombosis and/or
haemorrhage. Progression to a post -essential thrombocythaemia myelofibrosis stage
or transformation to acute myeloid leukaemia is rarely observed.;
A chronic myeloproliferative neoplasm that involves primarily the megakaryocytic lineage.
It is characterized by sustained thrombocytosis in the blood, increased numbers of
large, mature megakaryocytes in the bone marrow, and episodes of thrombosis and/or
haemorrhage. Progression to a post -essential thrombocythaemia myelofibrosis stage
or transformation to acute myeloid leukaemia is rarely observed.