ICD-11 code : 8B60.3;
Preferred Label : Progressive muscular atrophy;
ICD-11 definition : In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles
are present without upper motor neuron involvement. Over time, some patients may progress
to develop upper motor neuron signs, of which pathological evidence is common even
in patients who never displayed clinical upper motor neuron signs, suggesting that
progressive muscular atrophy is a form of ALS.;
ICD-11 synonym : progressive spinal muscle atrophy; progressive muscle atrophy; hereditary spinal muscle atrophy; pure progressive muscular atrophy; PMA - [progressive muscular atrophy];
ICD-11 acronym : PMA;
Origin ID : 1282359533;
Automatic exact mappings (from CISMeF team)
False automatic mappings
ICD-10 Mapping
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles
are present without upper motor neuron involvement. Over time, some patients may progress
to develop upper motor neuron signs, of which pathological evidence is common even
in patients who never displayed clinical upper motor neuron signs, suggesting that
progressive muscular atrophy is a form of ALS.