Preferred Label : Lipomatosis dolorosa;
ICD-11 definition : Lipomatosis dolorosa [Dercum disease] is a syndrome largely limited to obese middle-aged
women in which multiple painful subcutaneous fatty deposits develop in association
with easy bruisability and a symptom complex which includes psychiatric disturbances,
fatigue, weakness and musculoskeletal aches. The fatty deposits may be diffuse or
nodular in form and may be generalized, localized or juxta-articular in distribution.
Pain may be extreme and can occur spontaneously or as a response to pressure. Symptoms
tend to be poorly responsive to treatment. Some patients fulfil the criteria for fibromyalgia
and the distinction between the two syndromes is not always clear cut.;
ICD-11 synonym : Neurolipomatosis; Dercum disease; Adiposis dolorosa;
ICD-11 inclusion : Adiposis dolorosa;
Origin ID : 390869823;
Automatic exact mappings (from CISMeF team)
Lipomatosis dolorosa [Dercum disease] is a syndrome largely limited to obese middle-aged
women in which multiple painful subcutaneous fatty deposits develop in association
with easy bruisability and a symptom complex which includes psychiatric disturbances,
fatigue, weakness and musculoskeletal aches. The fatty deposits may be diffuse or
nodular in form and may be generalized, localized or juxta-articular in distribution.
Pain may be extreme and can occur spontaneously or as a response to pressure. Symptoms
tend to be poorly responsive to treatment. Some patients fulfil the criteria for fibromyalgia
and the distinction between the two syndromes is not always clear cut.
