Preferred Label : Concentric sclerosis;
ICD-11 definition : This is a demyelinating disorder with lesion(s) of concentric bands of demyelinated
and myelinated tissue. It is a variant of multiple sclerosis. Concentric sclerosis
is a primary inflammatory central nervous system demyelinating disease that is considered
a rare, radiographically and pathologically distinct variant of multiple sclerosis.
Characterised by demyelination occuring in concentrically arranged rings of partial
demyelination alternating with bands of demyelination.;
ICD-11 synonym : Greenfield's disease; encephalitis periaxialis concentrica; Baló disease; Baló; Baló sclerosis; Baló concentric sclerosis; Greenfield's disease (concentric sclerosis);
ICD-11 inclusion : encephalitis periaxialis;
Origin ID : 1387119224;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Validated automatic mappings to BTNT
This is a demyelinating disorder with lesion(s) of concentric bands of demyelinated
and myelinated tissue. It is a variant of multiple sclerosis. Concentric sclerosis
is a primary inflammatory central nervous system demyelinating disease that is considered
a rare, radiographically and pathologically distinct variant of multiple sclerosis.
Characterised by demyelination occuring in concentrically arranged rings of partial
demyelination alternating with bands of demyelination.