" /> Concentric sclerosis - CISMeF





Preferred Label : Concentric sclerosis;

ICD-11 definition : This is a demyelinating disorder with lesion(s) of concentric bands of demyelinated and myelinated tissue. It is a variant of multiple sclerosis. Concentric sclerosis is a primary inflammatory central nervous system demyelinating disease that is considered a rare, radiographically and pathologically distinct variant of multiple sclerosis. Characterised by demyelination occuring in concentrically arranged rings of partial demyelination alternating with bands of demyelination.;

ICD-11 synonym : Greenfield's disease; encephalitis periaxialis concentrica; Baló disease; Baló; Baló sclerosis; Baló concentric sclerosis; Greenfield's disease (concentric sclerosis);

ICD-11 inclusion : encephalitis periaxialis;

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This is a demyelinating disorder with lesion(s) of concentric bands of demyelinated and myelinated tissue. It is a variant of multiple sclerosis. Concentric sclerosis is a primary inflammatory central nervous system demyelinating disease that is considered a rare, radiographically and pathologically distinct variant of multiple sclerosis. Characterised by demyelination occuring in concentrically arranged rings of partial demyelination alternating with bands of demyelination.

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05/05/2025


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