Preferred Label : Merkel cell carcinoma of skin;
ICD-11 definition : A rare malignant cutaneous tumour seen in elderly patients. Its usual location is
on the head, neck and extremities. The tumour is composed of small round cells with
scanty cytoplasm arranged in a trabecular pattern, or in ill-defined nodules or in
a diffuse pattern. The tumour cells contain cytoplasmic membrane-bound dense core
granules resembling neurosecretory granules. There is strong evidence implicating
Merkel cell polyoma virus in a majority of cases of Merkel cell carcinoma.;
ICD-11 synonym : Merkel cell cancer; Neuroendocrine carcinoma of the skin;
ICD-11 inclusion : Merkel cell carcinoma of unspecified site;
Origin ID : 1020467726;
Automatic exact mappings (from CISMeF team)
A rare malignant cutaneous tumour seen in elderly patients. Its usual location is
on the head, neck and extremities. The tumour is composed of small round cells with
scanty cytoplasm arranged in a trabecular pattern, or in ill-defined nodules or in
a diffuse pattern. The tumour cells contain cytoplasmic membrane-bound dense core
granules resembling neurosecretory granules. There is strong evidence implicating
Merkel cell polyoma virus in a majority of cases of Merkel cell carcinoma.