Preferred Label : Splenic marginal zone lymphoma;
ICD-11 definition : A B-cell non-Hodgkin lymphoma composed of small lymphocytes which surround and replace
the splenic white pulp germinal centers. It involves the spleen and splenic hilar
lymph nodes, bone marrow, and often the peripheral blood. When lymphoma cells are
present in the peripheral blood, they are usually, but not always, characterized by
the presence of short polar villi.;
ICD-11 inclusion : Splenic lymphoma with circulating villous lymphocytes;
Origin ID : 1002343712;
Automatic exact mappings (from CISMeF team)
A B-cell non-Hodgkin lymphoma composed of small lymphocytes which surround and replace
the splenic white pulp germinal centers. It involves the spleen and splenic hilar
lymph nodes, bone marrow, and often the peripheral blood. When lymphoma cells are
present in the peripheral blood, they are usually, but not always, characterized by
the presence of short polar villi.
