ICD-11 code : 6D83;
Preferred Label : Frontotemporal dementia;
ICD-11 definition : Frontotemporal dementia (FTD) is a group of primary neurodegenerative disorders primarily
affecting the frontal and temporal lobes. Onset is typically insidious with a gradual
and worsening course. Several syndromic variants (some with an identified genetic
basis or familiality) are described that include presentations with predominantly
marked personality and behavioral changes (such as executive dysfunction, apathy,
deterioration of social cognition, repetitive behaviours, and dietary changes), predominantly
language deficits (that include semantic, agrammatic/nonfluent, and logopenic forms),
predominantly movement-related deficits (progressive supranuclear palsy, corticobasal
degeneration, multiple systems atrophy, or amyotrophic lateral sclerosis), or a combination
of these deficits. Memory function often remains relatively intact, particularly during
the early stages of the disorder.;
ICD-11 synonym : frontotemporal lobe dementia; temple dementia; FTD - [frontotemporal dementia]; dementia in fronto-temporal lobar degeneration;
ICD-11 acronym : FTD;
ICD-11 inclusion : frontal lobe dementia;
Origin ID : 831337417;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
Frontotemporal dementia (FTD) is a group of primary neurodegenerative disorders primarily
affecting the frontal and temporal lobes. Onset is typically insidious with a gradual
and worsening course. Several syndromic variants (some with an identified genetic
basis or familiality) are described that include presentations with predominantly
marked personality and behavioral changes (such as executive dysfunction, apathy,
deterioration of social cognition, repetitive behaviours, and dietary changes), predominantly
language deficits (that include semantic, agrammatic/nonfluent, and logopenic forms),
predominantly movement-related deficits (progressive supranuclear palsy, corticobasal
degeneration, multiple systems atrophy, or amyotrophic lateral sclerosis), or a combination
of these deficits. Memory function often remains relatively intact, particularly during
the early stages of the disorder.
