ICD-11 code : 2A42;
Preferred Label : Juvenile myelomonocytic leukaemia;
ICD-11 definition : A myelodysplastic/myeloproliferative neoplasm of childhood that is characterized by
proliferation principally of the granulocytic and monocytic lineages. Myelomonocytic
proliferation is seen in the bone marrow and the blood. The leukemic cells may infiltrate
any tissue, however liver, spleen, lymph nodes, skin, and respiratory tract are the
most common sites of involvement.;
ICD-11 synonym : juvenile myelomonocytic leukaemia without mention of remission;
ICD-11 "other" category code : 2A42.Y;
ICD-11 "unspecified" category code : 2A42.Z;
Origin ID : 1786015803;
UMLS CUI : C0349639;
Currated CISMeF NLP mapping
ICD-10 Mapping
Semantic type(s)
UMLS correspondences (same concept)
A myelodysplastic/myeloproliferative neoplasm of childhood that is characterized by
proliferation principally of the granulocytic and monocytic lineages. Myelomonocytic
proliferation is seen in the bone marrow and the blood. The leukemic cells may infiltrate
any tissue, however liver, spleen, lymph nodes, skin, and respiratory tract are the
most common sites of involvement.