Preferred Label :
respiratory broncholitis associated interstitial lung disease; RADLEX synonyms :
RB-ILD; respiratory broncholitis; respiratory broncholitis-associated interstitial lung disease; respiratory bronchiolitis-interstitial lung disease; Definition :
Pathology.—RB-ILD is a smoking-related disease characterized by inflammation (predominantly
by macrophages) of the respiratory bronchioles and peribronchiolar alveoli (5), sometimes
with elements of or overlap with nonspecific and desquamative interstitial pneumonias
(114). CT scans.—RB-ILD typically manifests as extensive centrilobular micronodules
and patchy ground-glass opacity corresponding to macrophage-rich alveolitis (Fig 60),
with or without fine fibrosis (115,116). It is often accompanied by bronchial wall
thickening and minor centrilobular emphysema. Areas of air trapping reflect a bronchiolitic
component. [Fleischner Society]; Image(s) :
RID5339Source :
Fleischner Society;
Origin ID : RID5339;
Automatic exact mappings (from CISMeF team)
Pathology.—RB-ILD is a smoking-related disease characterized by inflammation (predominantly
by macrophages) of the respiratory bronchioles and peribronchiolar alveoli (5), sometimes
with elements of or overlap with nonspecific and desquamative interstitial pneumonias
(114). CT scans.—RB-ILD typically manifests as extensive centrilobular micronodules
and patchy ground-glass opacity corresponding to macrophage-rich alveolitis (Fig 60),
with or without fine fibrosis (115,116). It is often accompanied by bronchial wall
thickening and minor centrilobular emphysema. Areas of air trapping reflect a bronchiolitic
component. [Fleischner Society]