Preferred Label : atypical teratoid rhabdoid tumor;
RADLEX synonyms : rhabdoid tumor; atypical teratoid-rhabdoid tumor (WHO grade IV);
Definition : A rare but highly lethal childhood tumor found almost exclusively in infants. Histopathologically,
it resembles rhabdomyosarcoma but the tumor cells are not of myogenic origin. Although
it arises primarily in the kidney, it may be found in other parts of the body. The
rhabdoid cytomorphology is believed to be the expression of a very primitive malignant
cell. (From Holland et al., Cancer Medicine, 3d ed, p2210) [MeSH];
RADLEX acronyms : ATRT;
UMLS CUI (RADLEX) : C0206743;
Origin ID : RID4424;
UMLS CUI : C1266184;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- Semantic type(s)
- UMLS correspondences (same concept)
A rare but highly lethal childhood tumor found almost exclusively in infants. Histopathologically,
it resembles rhabdomyosarcoma but the tumor cells are not of myogenic origin. Although
it arises primarily in the kidney, it may be found in other parts of the body. The
rhabdoid cytomorphology is believed to be the expression of a very primitive malignant
cell. (From Holland et al., Cancer Medicine, 3d ed, p2210) [MeSH]
