Preferred Label : supratentorial primitve neuroectodermal tumor;
RADLEX synonyms : PNET; cerebral medulloblastoma; cerebral ganglioneuroblastoma; cerebral neuroblastoma; supratentorial primitve neuroectodermal tumor (WHO grade IV);
Definition : A group of malignant tumors of the nervous system that feature primitive cells with
elements of neuronal and/or glial differentiation. Use of this term is limited by
some authors to central nervous system tumors and others include neoplasms of similar
origin which arise extracranially (i.e., neuroectodermal tumors, primitive, peripheral).
This term is also occasionally used as a synonym for medulloblastoma. In general,
these tumors arise in the first decade of life and tend to be highly malignant. (From
DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2059) [MeSH];
UMLS CUI (RADLEX) : C0206663;
Origin ID : RID4418;
UMLS CUI : C0206663;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to BTNT
Validated automatic mappings to NTBT
A group of malignant tumors of the nervous system that feature primitive cells with
elements of neuronal and/or glial differentiation. Use of this term is limited by
some authors to central nervous system tumors and others include neoplasms of similar
origin which arise extracranially (i.e., neuroectodermal tumors, primitive, peripheral).
This term is also occasionally used as a synonym for medulloblastoma. In general,
these tumors arise in the first decade of life and tend to be highly malignant. (From
DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2059) [MeSH]