Preferred Label : hemangioblastoma;
RADLEX synonyms : capillary hemangioblastoma;
Definition : A benign tumor of the nervous system that may occur sporadically or in association
with hippel-lindau disease. It accounts for approximately 2% of intracranial tumors,
arising most frequently in the cerebellar hemispheres and vermis. Histologically,
the tumors are composed of multiple capillary and sinusoidal channels lined with endothelial
cells and clusters of lipid-laden pseudoxanthoma cells. Usually solitary, these tumors
can be multiple and may also occur in the brain stem, spinal cord, retina, and supratentorial
compartment. Cerebellar hemangioblastomas usually present in the third decade with
intracranial hypertension, and ataxia. (From DeVita et al., Cancer: Principles and
Practice of Oncology, 5th ed, pp2071-2) [MeSH];
UMLS CUI (RADLEX) : C0206734;
Origin ID : RID3995;
UMLS CUI : C0206734;
Currated CISMeF NLP mapping
- Semantic type(s)
- UMLS correspondences (same concept)
A benign tumor of the nervous system that may occur sporadically or in association
with hippel-lindau disease. It accounts for approximately 2% of intracranial tumors,
arising most frequently in the cerebellar hemispheres and vermis. Histologically,
the tumors are composed of multiple capillary and sinusoidal channels lined with endothelial
cells and clusters of lipid-laden pseudoxanthoma cells. Usually solitary, these tumors
can be multiple and may also occur in the brain stem, spinal cord, retina, and supratentorial
compartment. Cerebellar hemangioblastomas usually present in the third decade with
intracranial hypertension, and ataxia. (From DeVita et al., Cancer: Principles and
Practice of Oncology, 5th ed, pp2071-2) [MeSH]
