Lipofibromatosis

Preferred Label : Lipofibromatosis;

NCIt synonyms : Infantile Fibromatosis, Non-Desmoid Type;

NCIt definition : A rare, slow-growing, painless tumor of infancy and early childhood that usually affects the distal extremities. It is characterized by the presence of alternating bands of mature adipose tissue and spindle-cell fibrous tissue, without destruction of the adipose tissue architecture. It does not metastasize, however the rate of local recurrences is high.;

Neoplastic status : Undetermined;

Details

Origin ID

C99180;

UMLS CUI

C3274592;

Automatic exact mappings (from CISMeF team)
- Lipofibromatosis [ICD-11 Extension code]
- Lipofibromatosis (morphologic abnormality) [SNOMED CT concept]
- infantile myofibromatosis [DO Concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Lipofibromatosis (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Nuclear Atypia [NCIt concept]
- Well-Circumscribed Lesion [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Fibroblast [NCIt concept]
- Neoplastic Spindle-Shaped Fibroblast [NCIt concept]
disease_has_finding
- Childhood Lesion [NCIt concept]
- Infiltrative Growth Pattern [NCIt concept]
- Locally Aggressive Lesion [NCIt concept]
- Low Mitotic Activity [NCIt concept]
- Slow Growing Painless Mass [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Fibroblast [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]

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