Preferred Label : Type III Total Anomalous Pulmonary Venous Return;
NCIt related terms : Type III (Infradiaphragmatic/Infracardiac) Total Anomalous Pulmonary Venous Return; Total Anomalous Pulmonary Venous Return, Type III (Infradiaphragmatic/Infracardiac); TAPVR Type III;
NCIt definition : Total anomalous pulmonary venous return in which the common pulmonary vein connects
to the portal venous system through the diaphragm.;
Alternative definition : NICHD: Total Anomalous Pulmonary Venous Return (TAPVR) is a rare congenital malformation
in which all four pulmonary veins do not connect normally to the left atrium, but
instead drain abnormally to the right atrium by way of an abnormal (anomalous) connection.
In type 3, infracardiac TAPVR, the pulmonary veins drain to the right atrium via the
hepatic (liver) veins and inferior vena cava. In this type, the pulmonary veins join
together behind the heart and then typically drain downwards, connecting to the liver's
portal vein system. They then drain through the vascular bed of the liver and enter
the right atrium from the hepatic veins.;
Origin ID : C98597;
UMLS CUI : C3274280;
Has associated anatomic sites
- Semantic type(s)
- concept_is_in_subset
