Preferred Label : Type I Total Anomalous Pulmonary Venous Return;
NCIt related terms : Total Anomalous Pulmonary Venous Return, Type I (Supracardiac); Type I (Supracardiac) Total Anomalous Pulmonary Venous Return; TAPVR Type I;
NCIt definition : Total anomalous pulmonary venous return in which the pulmonary veins drain into the
right atrium via the superior vena cava.;
Alternative definition : NICHD: Total Anomalous Pulmonary Venous Return (TAPVR) is a rare congenital malformation
in which all four pulmonary veins do not connect normally to the left atrium, but
instead drain abnormally to the right atrium by way of an abnormal (anomalous) connection.
In type 1, supracardiac TAPVR, the pulmonary veins drain to the right atrium via the
superior vena cava. In this type of TAPVR, the pulmonary veins come together behind
the heart and then drain upwards to an abnormal vertical vein. This vein joins the
innominate vein which connects to the right superior vena cava and drains to the right
atrium.;
Origin ID : C98590;
UMLS CUI : C3274273;
Has associated anatomic sites
- Semantic type(s)
- concept_is_in_subset
