" /> Hereditary Kidney Wilms Tumor - CISMeF





Preferred Label : Hereditary Kidney Wilms Tumor;

NCIt synonyms : Hereditary Kidney Adenosarcoma; Hereditary Renal Adenosarcoma; Familial Kidney Wilms Tumor; Hereditary Kidney Nephroblastoma;

NCIt related terms : Hereditary Wilms Tumor;

NCIt definition : Familial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0);

Neoplastic status : Malignant;

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31/07/2025


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