Preferred Label : Endometrioid Stromal and Related Neoplasms;
NCIt synonyms : Endometrioid Stromal and Related Tumors; Endometrial Stromal Neoplasm;
NCIt definition : A category of mesenchymal gynecologic neoplasms. It includes endometrial stromal nodule,
endometrioid stromal sarcoma, and undifferentiated sarcoma. Endometrial stromal nodule
has been described in the uterine corpus only. Histologically, it is characterized
by the lack of infiltration of the surrounding tissues. Endometrioid stromal sarcoma
affects the uterine corpus, and rarely, the ovaries, cervix, vagina, peritoneum, and
retroperitoneum. In the uterine corpus it is classified as low grade or high grade
endometrial stromal sarcoma. In the remainder of the anatomic sites it is classified
as low grade endometrioid stromal sarcoma. Undifferentiated sarcoma was previously
also known as high grade endometrial stromal sarcoma. In 2014, high grade endometrial
stromal sarcoma was reclassified and is currently considered a distinct and rare neoplasm
that affects the uterine corpus only. It appears to have a prognosis that falls between
low grade endometrial stromal sarcoma and undifferentiated sarcoma. The latter affects
the uterine corpus and rarely the remainder of the anatomic sites.;
Neoplastic status : Undetermined;
Origin ID : C8384;
UMLS CUI : C4287868;
Currated CISMeF NLP mapping
- Disease excludes normal cell origin
- Excludes anatomical site(s)
- Has associated anatomic sites
- Semantic type(s)
- Validated automatic mappings to BTNT
- disease_has_abnormal_cell
- disease_has_normal_cell_origin
- disease_has_normal_tissue_origin
