" /> Systemic EBV-Positive T-Cell Lymphoma of Childhood - CISMeF





Preferred Label : Systemic EBV-Positive T-Cell Lymphoma of Childhood;

NCIt synonyms : Systemic EBV-Positive T-Cell Lymphoproliferative Disorder of Childhood; Systemic Epstein-Barr Virus-Positive T-Cell Lymphoma of Childhood;

NCIt related terms : Systemic EBV-Positive T-Cell Lymphoproliferative Disease of Childhood;

NCIt definition : An aggressive and life-threatening, EBV-positive T-cell lymphoma affecting children. It is more prevalent in Taiwan and Japan. Clinically, it presents with acute onset of fever and generalized malaise, followed by hepatosplenomegaly and liver failure. Morphologically it is characterized by the presence of infiltrating T-lymphocytes which are usually small and erythrophagocytosis. Most patients have a fulminant clinical course.;

Alternative definition : NICHD: An aggressive, life-threatening, EBV-positive T-cell lymphoproliferative disorder affecting children.;

Neoplastic status : Malignant;

ICD-O code : 9724/3;

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01/05/2024


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