Pediatric Nodal Marginal Zone Lymphoma

Preferred Label : Pediatric Nodal Marginal Zone Lymphoma;

NCIt synonyms : Childhood Nodal Marginal Zone Lymphoma;

NCIt definition : A nodal marginal zone lymphoma affecting the pediatric population, predominantly males. It presents with asymptomatic and localized (mainly head and neck) disease in the vast majority of cases. Morphologically there is often progressive transformation of the germinal centers. The prognosis is excellent.;

Alternative definition : NICHD: A nodal marginal zone lymphoma affecting the pediatric population, predominantly males. It presents with asymptomatic and localized (mainly head and neck) disease in the vast majority of cases.;

Neoplastic status : Malignant;

Concept status : Provisional_Concept;

Details

Origin ID

C80299;

UMLS CUI

C2698751;

Automatic exact mappings (from CISMeF team)
- Pediatric nodal marginal zone lymphoma (morphologic abnormality) [SNOMED CT concept]
Disease excludes abnormal cell
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor B-Lymphoblast [NCIt concept]
Disease may have findings
- Localized Disease [NCIt concept]
- Progressive Transformation of Germinal Centers [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Pediatric nodal marginal zone lymphoma (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- NCIt Neoplasm Core Terminology [NCIt concept]
- NICHD Terminology [NCIt concept]
- Pediatric Hematology-Oncology Terminology [NCIt concept]
disease_excludes_finding
- Aggressive Clinical Course [NCIt concept]
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Centrocyte-Like Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
disease_has_finding
- Childhood Lesion [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Heavy Chain Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Kappa Light Chain Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Lambda Light Chain Gene Rearrangement [NCIt concept]
disease_has_normal_cell_origin
- B-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Marginal Zone B-Lymphocyte [NCIt concept]
- Marginal Zone B-Lymphocyte of Nodal Type [NCIt concept]
- Mature B-Lymphocyte [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
- Marginal Zone [NCIt concept]
- Marginal Zone of the Lymph Node [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymph Node [NCIt concept]
- Lymphatic System [NCIt concept]
disease_may_have_abnormal_cell
- Neoplastic Monocytoid B-Lymphocyte [NCIt concept]
- Neoplastic Plasma Cell [NCIt concept]

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