Childhood Pleomorphic Rhabdomyosarcoma

Preferred Label : Childhood Pleomorphic Rhabdomyosarcoma;

NCIt synonyms : Pediatric Pleomorphic Rhabdomyosarcoma; Pleomorphic Childhood Rhabdomyosarcoma;

NCIt related terms : Childhood Anaplastic Rhabdomyosarcoma; Pleomorphic Rhabdomyosarcoma;

NCIt definition : A rare aggressive rhabdomyosarcoma occurring in children. The neoplasm is characterized by the presence of bizarre round, spindle, and polygonal cells.;

Alternative definition : NICHD: A pleomorphic rhabdomyosarcoma occurring in children.;

Neoplastic status : Malignant;

Details

Origin ID

C7959;

UMLS CUI

C0279614;

Automatic exact mappings (from CISMeF team)
- Pleomorphic rhabdomyosarcoma [PASCAL descriptor]
- Pleomorphic rhabdomyosarcoma [ORDO Disease]
- Pleomorphic rhabdomyosarcoma [ICD-9 code]
- Pleomorphic rhabdomyosarcoma (disorder) [SNOMED CT concept]
- Pleomorphic rhabdomyosarcoma (morphologic abnormality) [SNOMED CT concept]
- childhood pleomorphic rhabdomyosarcoma [DO Concept]
- pleomorphic rhabdomyosarcoma [DO Concept]
- pleomorphic rhabdomyosarcoma [SNOMED Notion]
DO Cross reference
- childhood pleomorphic rhabdomyosarcoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Musculoskeletal System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- childhood pleomorphic rhabdomyosarcoma [DO Concept]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- NICHD Terminology [NCIt concept]
- Pediatric Hematology-Oncology Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Bizarre Cell with Evidence of Skeletal Muscle Differentiation [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Rhabdomyoblast [NCIt concept]
- Malignant Skeletal Muscle Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Muscle Cell [NCIt concept]
- Neoplastic Skeletal Muscle Cell [NCIt concept]
disease_has_finding
- Childhood Lesion [NCIt concept]
- High Grade Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Nuclear Pleomorphism [NCIt concept]
- Rapidly Enlarging Mass [NCIt concept]
- Severe Cytologic Atypia [NCIt concept]
- Well-Circumscribed Lesion [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Muscle Cell [NCIt concept]
- Skeletal Muscle Cell [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Muscle Tissue [NCIt concept]
- Skeletal Muscle Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_may_have_molecular_abnormality
- FGFR4 Gene Mutation [NCIt concept]

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