NCIt definition : An aggressive malignant mesenchymal neoplasm arising from skeletal muscle in children.
Only a small percentage of tumors arise in the skeletal muscle of the extremities.
The majority arise in other anatomic sites.;
Alternative definition : NICHD: An aggressive, malignant, mesenchymal neoplasm arising from skeletal muscle
in children; the most common sites are the head, the genitourinary tract, and the
extremities.;