Follicular Helper T-Cell Lymphoma, Angioimmunoblastic-Type

Preferred Label : Follicular Helper T-Cell Lymphoma, Angioimmunoblastic-Type;

NCIt synonyms : Angioimmunoblastic Lymphadenopathy with Dysproteinemia; Angioimmunoblastic Lymphadenopathy; Angioimmunoblastic Lymphadenopathy Type T-Cell Lymphoma; AILD; Follicular Helper T-Cell Lymphoma, Angioimmunoblastic Type (Angioimmunoblastic T-Cell Lymphoma); AITL;

NCIt related terms : Angioimmunoblastic T-Cell Lymphoma;

NCIt definition : An aggressive follicular helper T-cell lymphoma affecting lymph nodes and other sites. It is characterized by a polymorphous infiltrate and prominent proliferation of high endothelial venules and follicular dendritic cells. It is associated with EBV infection and affects mainly older adults.;

Alternative definition : NCI-GLOSS: An aggressive (fast-growing) type of T-cell non-Hodgkin lymphoma marked by enlarged lymph nodes and hypergammaglobulinemia (increased antibodies in the blood). Other symptoms may include a skin rash, fever, weight loss, or night sweats.;

Neoplastic status : Malignant;

ICD-O code : 9767/1; 9705/3;

Codes from synonyms : CDR0000346464; C86.5;

Details

Origin ID

C7528;

UMLS CUI

C0020981;

Currated CISMeF NLP mapping
- Angioimmunoblastic T-cell lymphoma [ICD-10 Sub-category]
- Angioimmunoblastic T-cell lymphoma [ICD-11 Subcategory]
- Angioimmunoblastic T-cell lymphoma [MedDRA Preferred Term]
- Angioimmunoblastic T-cell lymphoma [ICD-O code]
- Angioimmunoblastic T-cell lymphoma [ORDO Disease]
- Angioimmunoblastic T-cell lymphoma (disorder) [SNOMED CT concept]
- Angioimmunoblastic T-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- Angioimmunoblastic T-cell lymphoma NOS [MedDRA LLT]
- Angioimmunoblastic T-cell lymphomas [MedDRA High Level Term]
- Angioimmunoblastic lymphadenopathy [MedDRA LLT]
- Angioimmunoblastic lymphadenopathy (AIL) [ICD-11 Extension code]
- Angioimmunoblastic lymphadenopathy (morphologic abnormality) [SNOMED CT concept]
- Immunoblastic lymphadenopathy [PASCAL descriptor]
- angioimmunoblastic T cell lymphoma [Disease (Nov.)]
- angioimmunoblastic T-cell lymphoma [DO Concept]
- angioimmunoblastic lymphadenopathy [SNOMED Notion]
- immunoblastic lymphadenopathy [MeSH Descriptor]
- immunoblastic lymphadenopathy [MeSH concept]
- peripheral t-cell lymphoma, aild (angioimmunoblastic lymphadenopathy with dysproteinemia) [SNOMED Notion]
DO Cross reference
- angioimmunoblastic T-cell lymphoma [DO Concept]
Disease excludes abnormal cell
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Hepatomegaly [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Skin Rash [NCIt concept]
- Splenomegaly [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Angioimmunoblastic T-cell lymphoma [ICD-O code]
- Angioimmunoblastic T-cell lymphoma [ICD-10 Sub-category]
- Angioimmunoblastic T-cell lymphoma [ORDO Disease]
- Angioimmunoblastic T-cell lymphoma [ICD-11 Subcategory]
- Angioimmunoblastic T-cell lymphoma [MedDRA Preferred Term]
- Angioimmunoblastic T-cell lymphoma (disorder) [SNOMED CT concept]
- Angioimmunoblastic T-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- Angioimmunoblastic T-cell lymphoma NOS [MedDRA LLT]
- Angioimmunoblastic T-cell lymphomas [MedDRA High Level Term]
- Angioimmunoblastic lymphadenopathy [MedDRA LLT]
- Angioimmunoblastic lymphadenopathy (morphologic abnormality) [SNOMED CT concept]
- Angioimmunoblastic lymphadenopathy with dysproteinaemia [MedDRA LLT]
- Angioimmunoblastic lymphadenopathy with dysproteinemia [MedDRA LLT]
- angioimmunoblastic T cell lymphoma [Disease (Nov.)]
- angioimmunoblastic T-cell lymphoma [DO Concept]
- angioimmunoblastic lymphadenopathy [SNOMED Notion]
- immunoblastic lymphadenopathy [MeSH Descriptor]
- immunoblastic lymphadenopathy [MeSH concept]
- peripheral t-cell lymphoma, aild (angioimmunoblastic lymphadenopathy with dysproteinemia) [SNOMED Notion]
concept_is_in_subset
- CPTAC Codelists Terminology [NCIt concept]
- CPTAC Neoplasms Codelist [NCIt concept]
- CPTAC Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Elixhauser Lymphoma Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic Small to Medium-Sized T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- Malignant Cellular Infiltrate [NCIt concept]
- Neoplastic Cells with TFH Cell Phenotype Present [NCIt concept]
- Polymorphic Cellular Infiltrate [NCIt concept]
- Proliferation of Follicular Dendritic Cells Present [NCIt concept]
- Proliferation of High Endothelial Venules Present [NCIt concept]
disease_has_normal_cell_origin
- CD4-Positive T-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymph Node [NCIt concept]
- Lymphatic System [NCIt concept]
disease_may_have_abnormal_cell
- Neoplastic Medium-Sized T-Lymphocyte [NCIt concept]
- Neoplastic T-Immunoblast [NCIt concept]
- Neoplastic T-Lymphocyte with Clear Cytoplasm [NCIt concept]
- Reed-Sternberg-Like Cell [NCIt concept]
disease_may_have_associated_disease
- EBV Infection [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Gain of Chromosome X [NCIt concept]
- Trisomy 3 [NCIt concept]
- Trisomy 5 [NCIt concept]
disease_may_have_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
- DNMT3A Gene Mutation [NCIt concept]
- IDH2 Gene Mutation [NCIt concept]
- RHOA Gene Mutation [NCIt concept]
- TET2 Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

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