Papillary Intralymphatic Angioendothelioma

Preferred Label : Papillary Intralymphatic Angioendothelioma;

NCIt synonyms : Papillary Endovascular Angioendothelioma; Malignant Endothelial Papillary Angioendothelioma; PILA;

NCIt related terms : Dabska tumor; Endovascular papillary angioendothelioma;

NCIt definition : A rare, intermediate and rarely metastasizing blood vessel neoplasm that most often affects the skin and soft tissue of the extremities and manifests as a slow-growing induration, nodule, or plaque. Rare cases have been described in the spleen, tongue, and testis as well. It is characterized by the presence of lymphatic-like vascular channels and papillary endothelial proliferation.;

Neoplastic status : Undetermined;

ICD-O code : 9135/1;

Details

Origin ID

C7526;

UMLS CUI

C0346087;

Automatic exact mappings (from CISMeF team)
- Papillary intralymphatic angioendothelioma [ICD-11 Extension code]
- Pila (organism) [SNOMED CT concept]
- Primary intralymphatic angioendothelioma [ORDO Disease]
Currated CISMeF NLP mapping
- Endovascular papillary angioendothelioma [ICD-O code]
- Papillary intralymphatic angioendothelioma (morphologic abnormality) [SNOMED CT concept]
- endovascular papillary angioendothelioma [Radlex concept]
Disease may have findings
- Skin Nodule [NCIt concept]
- Skin Plaque [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
False automatic mappings
- Papillary intralymphatic angioendothelioma of childhood (disorder) [SNOMED CT concept]
Has associated anatomic sites
- Cardiovascular System [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Vascular System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Endovascular papillary angioendothelioma [ICD-O code]
- Papillary intralymphatic angioendothelioma (disorder) [SNOMED CT concept]
- Papillary intralymphatic angioendothelioma (morphologic abnormality) [SNOMED CT concept]
- endovascular papillary angioendothelioma [Radlex concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- High Grade Lesion [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Endothelial Cell [NCIt concept]
- Neoplastic Plump Endothelial Cell [NCIt concept]
disease_has_finding
- Intravascular Papillary Endothelial Hyperplasia [NCIt concept]
- Locally Aggressive Lesion [NCIt concept]
- Rarely Metastasizing Lesion [NCIt concept]
- Vascular Channel Formation [NCIt concept]
disease_has_normal_cell_origin
- Endothelial Cell [NCIt concept]
disease_has_normal_tissue_origin
- Blood Vessel Endothelium [NCIt concept]
- Soft Tissue [NCIt concept]
- Vascular Endothelium [NCIt concept]
disease_has_primary_anatomic_site
- Blood Vessel [NCIt concept]
- Vascular System [NCIt concept]

Keyword's position in hierarchy(ies) :

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