Primary Cutaneous Marginal Zone Lymphoproliferative Disorder - CISMeF
Primary Cutaneous Marginal Zone Lymphoproliferative DisorderNCIt concept
Preferred Label : Primary Cutaneous Marginal Zone Lymphoproliferative Disorder;
NCIt synonyms : Marginal Zone B Cell Lymphoma of the Skin; Primary Cutaneous Marginal Zone B-Cell Lymphoma of Mucosa-Associated Lymphoid Tissue; Skin-Associated Lymphoid Tissue Lymphoma; Primary Cutaneous Marginal Zone B Cell Lymphoma of Mucosa-Associated Lymphoid Tissue; SALT Lymphoma; C-MALT; Marginal Zone B Cell Lymphoma of Skin; Cutaneous Marginal Zone B Cell Lymphoma of Mucosa-Associated Lymphoid Tissue; Cutaneous Immunocytoma; PCMZL; Primary Cutaneous Marginal Zone Lymphoma of Mucosa-Associated Lymphoid Tissue;
NCIt definition : A B-cell lymphoproliferative disorder that arises from the skin. It was previously
known as primary cutaneous marginal zone lymphoma of mucosa-associated lymphoid tissue.
Two subtypes are recognized: heavy chain class-switched primary cutaneous marginal
zone lymphoproliferative disorder and IgM-positive primary cutaneous marginal zone
lymphoproliferative disorder. The majority of cases are class-switched and predominantly
IgG-positive.;