Primary Cutaneous Follicle Center Lymphoma

Preferred Label : Primary Cutaneous Follicle Center Lymphoma;

NCIt synonyms : Cutaneous Follicle Center Lymphoma; Reticulohistiocytoma of the Dorsum; Cutaneous Follicle Centre Lymphoma; Crosti's Disease; PCFCL;

NCIt related terms : Cutaneous follicle center lymphoma, unspecified site;

NCIt definition : A primary lymphoma of the skin composed of various numbers of small and large irregular neoplastic follicle center cells. Its morphologic pattern can be nodular, diffuse, or nodular and diffuse. It presents with solitary or grouped plaques and tumors, and it usually involves the scalp, forehead, or trunk. It rarely involves the legs. This type of cutaneous lymphoma tends to remain localized to the skin.;

Neoplastic status : Malignant;

ICD-O code : 9597/3;

Codes from synonyms : C82.60;

Details

Origin ID

C7217;

UMLS CUI

C1333171;

Currated CISMeF NLP mapping
- Cutaneous follicle center lymphoma [ICD-10 Sub-category]
- Primary cutaneous follicle center cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- Primary cutaneous follicle center lymphoma [ORDO Disease]
Disease excludes abnormal cell
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor B-Lymphoblast [NCIt concept]
Disease may have findings
- Diffuse Pattern [NCIt concept]
- Localized Disease [NCIt concept]
- Nodular Pattern [NCIt concept]
- Nodular and Diffuse Pattern [NCIt concept]
- Skin Nodule [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Primary cutaneous follicle center cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- Primary cutaneous follicle center lymphoma [ORDO Disease]
- Primary cutaneous follicle centre lymphoma [ICD-11 Subcategory]
- Primary cutaneous follicular center B-cell lymphoma (disorder) [SNOMED CT concept]
Validated automatic mappings to BTNT
- Primary cutaneous follicular center B-cell lymphoma (disorder) [SNOMED CT concept]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Elixhauser Lymphoma Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Aggressive Clinical Course [NCIt concept]
- Benign Cellular Infiltrate [NCIt concept]
disease_excludes_molecular_abnormality
- IRF4/MUM1 Messenger RNA Overexpression [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Multilobated Neoplastic B-Lymphocyte [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Follicle Center B-Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Large Cleaved Follicle Center Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic Small Cleaved Follicle Center Cell [NCIt concept]
disease_has_finding
- Cutaneous Involvement [NCIt concept]
- Extranodal Disease [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Heavy Chain Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Kappa Light Chain Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Lambda Light Chain Gene Rearrangement [NCIt concept]
disease_has_normal_cell_origin
- B-Lymphocyte [NCIt concept]
- Germinal Center B-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Mature B-Lymphocyte [NCIt concept]
disease_has_normal_tissue_origin
- Germinal Center [NCIt concept]
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_abnormal_cell
- Neoplastic Centroblast [NCIt concept]

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