Blastic Plasmacytoid Dendritic Cell Neoplasm

Preferred Label : Blastic Plasmacytoid Dendritic Cell Neoplasm;

NCIt synonyms : Agranular CD4 CD56 Hematodermic Neoplasm/Tumor; CD4 /CD56 Hematodermic Neoplasm; BPDCN; Blastic Natural Killer Leukemia/Lymphoma; Agranular CD4 Natural Killer Cell Leukemia; Monomorphic NK-Cell Lymphoma; Blastic NK Cell Lymphoma;

NCIt related terms : Blastic NK-cell lymphoma;

NCIt definition : A clinically aggressive neoplasm derived from the precursors of plasmacytoid dendritic cells (also called professional type I interferon-producing cells or plasmacytoid monocytes), with a high frequency of cutaneous and bone marrow involvement and leukemic dissemination. (WHO 2017);

Neoplastic status : Malignant;

ICD-O code : 9727/3;

Codes from synonyms : C86.4;

Details

Origin ID

C7203;

UMLS CUI

C1301363;

Automatic exact mappings (from CISMeF team)
- Blastic NK cell lymphoma [ICD-11 More detail]
- Blastic NK-cell lymphoma [ICD-10 Sub-category]
- Blastic plasmacytoid dendritic cell neoplasm [ICD-11 More detail]
CISMeF manual mappings
- Blastic plasmacytoid dendritic cell neoplasm (morphologic abnormality) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Blastic NK-cell lymphoma (morphologic abnormality) [Inactive SNOMED CT concept]
- Blastic plasmacytoid dendritic cell neoplasm [ICD-11 Subcategory]
- Blastic plasmacytoid dendritic cell neoplasm (disorder) [SNOMED CT concept]
- CD4+/CD56+ hematodermic neoplasm [ORDO Disease]
- blastic NK cell lymphoma [Disease (Nov.)]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Widespread Disease [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Blastic NK-cell lymphoma [ICD-10 Sub-category]
- Blastic NK-cell lymphoma (morphologic abnormality) [Inactive SNOMED CT concept]
- Blastic plasmacytoid dendritic cell neoplasm [ICD-11 Subcategory]
- Blastic plasmacytoid dendritic cell neoplasm (disorder) [SNOMED CT concept]
- Blastic plasmacytoid dendritic cell neoplasm (morphologic abnormality) [SNOMED CT concept]
- CD4+/CD56+ hematodermic neoplasm [ORDO Disease]
- blastic NK cell lymphoma [Disease (Nov.)]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Elixhauser Lymphoma Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_has_abnormal_cell
- CD4+/CD56+ Neoplastic Medium-Sized Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
disease_has_finding
- CD4-Positive Neoplastic Cells Present [NCIt concept]
- CD56-Positive Neoplastic Cells Present [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Histiocytosis [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
- Skin Nodule [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
- Plasmacytoid Dendritic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients