Acquired Pure Red Cell Aplasia

Preferred Label : Acquired Pure Red Cell Aplasia;

NCIt definition : A disease characterized by normocytic, normochromic anemia, low hematocrit, reticulocytopenia and selective erythroid hypoplasia. It can occur as a chronic or acute form; the former is predominantly seen in adults and the latter in children. Pathogenesis involves immune dysfunction with antibodies directed against erythroid precursor cells or erythropoietin, or due to T-cell mediated suppression of erythropoiesis.;

Alternative definition : NCI-GLOSS: A rare disorder in which the bone marrow makes almost no red blood cells. It may be caused by infection or by certain drugs. Patients with this disorder may also have a thymoma (a tumor of the thymus) or an autoimmune condition such as lupus erythematosus or rheumatoid arthritis.; NICHD: A disease characterized by normocytic, normochromic anemia, low hematocrit, reticulocytopenia, and selective erythroid hypoplasia. It can occur as a chronic or acute form; the former is predominantly seen in adults, and the latter in children.;

Codes from synonyms : CDR0000672833;

Details

Origin ID

C70548;

UMLS CUI

C0340961;

Currated CISMeF NLP mapping
- Acquired pure red cell aplasia [ICD-11 Category]
- Acquired pure red cell aplasia [erythroblastopenia] [ICD-10 category]
- Pure red cell aplasia, acquired (disorder) [SNOMED CT concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Acquired pure red cell aplasia [ICD-11 Category]
- Acquired pure red cell aplasia [erythroblastopenia] [ICD-10 category]
- Acquired pure red cell aplasia, unspecified [ICD-10 Sub-category]
- Acquired pure red cell aplasia, unspecified [ICD-10 Sub-category (who)]
- Acquired red cell aplasia (disorder) [SNOMED CT concept]
- Pure red cell aplasia, acquired (disorder) [SNOMED CT concept]
Validated automatic mappings to BTNT
- Acquired pure red cell aplasia, unspecified [ICD-10 Sub-category (who)]
- Acquired pure red cell aplasia, unspecified [ICD-10 Sub-category]
Validated automatic mappings to NTBT
- Acquired red cell aplasia (disorder) [SNOMED CT concept]
concept_is_in_subset
- NICHD Terminology [NCIt concept]
- Pediatric Hematology-Oncology Terminology [NCIt concept]
disease_has_finding
- Marked Reduction or Absence of Erythroid Precursors in the Bone Marrow [NCIt concept]
- Reticulocytopenia [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]

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