Cystic Partially Differentiated Kidney Nephroblastoma

Preferred Label : Cystic Partially Differentiated Kidney Nephroblastoma;

NCIt synonyms : Malignant Cystic Nephroma;

NCIt related terms : Malignant multilocular cystic nephroma; Cystic partially differentiated nephroblastoma;

NCIt definition : A variant of Wilms tumor of the kidney characterized by the presence of cystic spaces separated by septa. The septa contain immature epithelial cells, immature stromal cells, and blastema cells. Surgical resection is usually curative.;

Alternative definition : NICHD: A rare, cystic variant of Wilms tumor wholly comprising cysts in which their thin septa form the only solid portion of the tumor.;

Neoplastic status : Malignant;

ICD-O code : 8959/1; 8959/3;

Details

Origin ID

C6897;

UMLS CUI

C1266139;

Disease excludes abnormal cell
- Neoplastic Glial Cell [NCIt concept]
Disease excludes normal cell origin
- Glial Cell [NCIt concept]
Disease may have findings
- Abdominal Mass [NCIt concept]
- Abdominal Pain [NCIt concept]
- Hematuria [NCIt concept]
- Hypertension [NCIt concept]
Has associated anatomic sites
- Genitourinary System [NCIt concept]
- Kidney [NCIt concept]
- Kidney and Ureter [NCIt concept]
- Urinary System [NCIt concept]
See also inter- (CISMeF)
- Malignant cystic nephroma (morphologic abnormality) [SNOMED CT concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Cystic partially differentiated nephroblastoma [ICD-O code]
- Cystic partially differentiated nephroblastoma [Disease (Nov.)]
- Cystic partially differentiated nephroblastoma (morphologic abnormality) [SNOMED CT concept]
- Cystic partially differentiated nephroblastoma of kidney (disorder) [SNOMED CT concept]
- Malignant cystic nephroma (disorder) [SNOMED CT concept]
- Malignant cystic nephroma (morphologic abnormality) [SNOMED CT concept]
- cystic partially differentiated nephroblastoma [Radlex concept]
Validated automatic mappings to NTBT
- Malignant cystic nephroma [ICD-O code]
- Malignant cystic nephroma [ICD-11 Extension code]
- Malignant cystic nephroma (disorder) [SNOMED CT concept]
- malignant cystic nephroma [DO Concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NICHD Terminology [NCIt concept]
- Pediatric Hematology-Oncology Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_excludes_molecular_abnormality
- DICER1 Gene Mutation [NCIt concept]
disease_excludes_normal_tissue_origin
- Germinal Layer [NCIt concept]
disease_has_abnormal_cell
- Malignant Blastemal Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Childhood Lesion [NCIt concept]
- Cystic Change [NCIt concept]
- Cystic Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Mixed Cellular Population [NCIt concept]
- Multilocular Lesion [NCIt concept]
- Well-Circumscribed Lesion [NCIt concept]
disease_has_normal_cell_origin
- Blastemal Cell [NCIt concept]
- Cell [NCIt concept]
- Embryonic Cell [NCIt concept]
- Nephrogenic Blastemal Cell [NCIt concept]
disease_has_normal_tissue_origin
- Embryonic Tissue [NCIt concept]
- Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Kidney [NCIt concept]
disease_mapped_to_chromosome
- Human Chromosome 11 [NCIt concept]
disease_mapped_to_gene
- WT1 Gene [NCIt concept]
disease_may_have_molecular_abnormality
- Inactivating WT1 Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients