Meningeal Melanocytosis

Preferred Label : Meningeal Melanocytosis;

NCIt synonyms : Diffuse Melanosis; Diffuse Meningeal Melanocytosis; Diffuse Melanocytosis;

NCIt definition : A diffuse or multifocal proliferation of uniform nevoid polygonal cells in the leptomeninges. Cells may spread into the Virchow-Robin spaces without frank invasion of the brain. Diffuse melanocytosis carries a poor prognosis even in the absence of histologic malignancy. (WHO);

Neoplastic status : Malignant;

ICD-O code : 8728/0;

Details

Origin ID

C6890;

UMLS CUI

C1266112;

Automatic exact mappings (from CISMeF team)
- Diffuse melanocytosis [ICD-O code]
- Diffuse melanocytosis [ICD-11 Extension code]
- Meningeal melanocytosis [ICD-11 Extension code]
- diffuse meningeal melanocytosis [DO Concept]
DO Cross reference
- diffuse meningeal melanocytosis [DO Concept]
Disease may have findings
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- S-100-Positive Neoplastic Cells Present [NCIt concept]
- Seizure [NCIt concept]
Has associated anatomic sites
- Central Nervous System [NCIt concept]
- Leptomeninges [NCIt concept]
- Meninges [NCIt concept]
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Diffuse melanocytosis (morphologic abnormality) [SNOMED CT concept]
- diffuse meningeal melanocytosis [DO Concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Indolent Clinical Course [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Melanocyte [NCIt concept]
- Nevoid Polygonal Cell [NCIt concept]
disease_has_finding
- Diffuse Lesion [NCIt concept]
- Primary Lesion [NCIt concept]
disease_has_normal_cell_origin
- Melanocyte [NCIt concept]
disease_has_normal_tissue_origin
- Leptomeninges [NCIt concept]
disease_has_primary_anatomic_site
- Central Nervous System [NCIt concept]
- Meninges [NCIt concept]
disease_may_have_molecular_abnormality
- BRAF Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

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