Endolymphatic Sac Tumor

Preferred Label : Endolymphatic Sac Tumor;

NCIt synonyms : Aggressive Papillary Tumor of the Temporal Bone; ELST; Low-Grade Papillary Adenocarcinoma of Endolymphatic Sac Origin; Heffner Tumor; Low Grade Papillary Adenocarcinoma of Endolymphatic Sac Origin;

CISMeF acronym : ELST;

NCIt definition : A rare, low-grade malignant epithelial tumor arising from the endolymphatic sac in the temporal bone. Morphologically, it is characterized by the presence of papillary and cystic structures. As tumors grow, they may destroy petrous temporal bone and extend into the middle ear and the middle and posterior cranial fossae and into the cerebellopontine angle. (WHO 2017);

Neoplastic status : Malignant;

ICD-O code : 8260/1;

Details

Origin ID

C67560;

UMLS CUI

C2348239;

Automatic exact mappings (from CISMeF team)
- Endolymphatic sac tumor [ICD-11 Extension code]
CISMeF manual mappings
- Neoplasm of endolymphatic sac (disorder) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Endolymphatic sac tumor [HPO term]
- endolymphatic sac tumor [Radlex concept]
- endolymphatic sac tumour [Disease (Nov.)]
Disease excludes abnormal cell
- Malignant Squamous Cell [NCIt concept]
- Malignant Stromal Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
- Neoplastic Squamous Cell [NCIt concept]
Excludes anatomical site(s)
- Extrahepatic Bile Duct [NCIt concept]
- Intrahepatic Bile Duct [NCIt concept]
Has associated anatomic sites
- Ear [NCIt concept]
- Head and Neck [NCIt concept]
- Inner Ear [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Endolymphatic sac tumor [HPO term]
- Neoplasm of endolymphatic sac (disorder) [SNOMED CT concept]
- endolymphatic sac tumor [Radlex concept]
- endolymphatic sac tumour [Disease (Nov.)]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Mixed Neoplastic Glandular and Squamous Cell Population [NCIt concept]
- Mucoid Stroma Formation [NCIt concept]
- Pseudopapillary Pattern [NCIt concept]
disease_has_abnormal_cell
- Adenocarcinoma Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Epithelial Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
- Neoplastic Glandular Cell [NCIt concept]
disease_has_finding
- Carcinomatous Component Present [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Papillary Growth Pattern [NCIt concept]
disease_has_grade
- Low Grade [NCIt concept]
disease_has_normal_cell_origin
- Epithelial Cell [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Inner Ear [NCIt concept]

Keyword's position in hierarchy(ies) :

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