Rosette-Forming Glioneuronal Tumor of the Fourth Ventricle

Preferred Label : Rosette-Forming Glioneuronal Tumor of the Fourth Ventricle;

NCIt definition : A central nervous system neoplasm arising from the fourth ventricle. It is characterized by the presence of neurocytes forming pseudorosettes and astrocytes which contain Rosenthal fibers. Cytologic atypia is minimal.;

Neoplastic status : Undetermined;

ICD-O code : 0000/0; 9509/1;

Details

Origin ID

C67559;

UMLS CUI

C2347979;

Automatic exact mappings (from CISMeF team)
- Rosette-forming glioneuronal tumor [ORDO Disease]
Disease excludes normal cell origin
- Oligodendrocyte [NCIt concept]
Excludes anatomical site(s)
- Spinal Cord [NCIt concept]
Has associated anatomic sites
- Brain [NCIt concept]
- Central Nervous System [NCIt concept]
- Nervous System [NCIt concept]
- Supratentorial Brain [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
Validated automatic mappings to NTBT
- Rosette-forming glioneuronal tumor [HPO term]
concept_is_in_subset
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Precise Histogenesis Unknown [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Astrocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Neuroepithelial Cell [NCIt concept]
- Neoplastic Neuroepithelial Cell and Neoplastic Perineural Cell [NCIt concept]
disease_has_finding
- Pseudorosette Formation [NCIt concept]
- Rosenthal Fibers Present [NCIt concept]
disease_has_molecular_abnormality
- FGFR1 Gene Mutation [NCIt concept]
disease_has_normal_cell_origin
- Neuroepithelial Cell [NCIt concept]
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
disease_has_normal_tissue_origin
- Nerve Tissue, Neuroepithelial Tissue, and Nerve Sheaths [NCIt concept]
- Neuroepithelial Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Brain [NCIt concept]
- Central Nervous System [NCIt concept]
- Fourth Ventricle [NCIt concept]
disease_may_have_molecular_abnormality
- PIK3CA Gene Mutation [NCIt concept]
- PIK3R1 Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

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