" /> Malignant Peripheral Nerve Sheath Tumor with Perineurial Differentiation - CISMeF





Preferred Label : Malignant Peripheral Nerve Sheath Tumor with Perineurial Differentiation;

Obsolete resource : true;

NCIt synonyms : Malignant Perineurioma; Perineurial Malignant Peripheral Nerve Sheath Tumor;

NCIt related terms : Perineural MPNST; Perineurioma, malignant;

NCIt definition : A very rare malignant tumor with morphologic features similar to those of benign perineurioma of soft tissue along with hypercellularity, nuclear atypia, hyperchromasia, and a high mitotic rate.;

NCIt note : See 'Malignant Perineurioma(C207066)';

Neoplastic status : Malignant;

Concept status : Retired_Concept;

ICD-O code : 9571/3;

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31/07/2025


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