Epithelioid Malignant Peripheral Nerve Sheath Tumor

Preferred Label : Epithelioid Malignant Peripheral Nerve Sheath Tumor;

NCIt synonyms : Malignant Epithelioid Neoplasm of Peripheral Nerve Sheath; Malignant Epithelioid Neoplasm of the Peripheral Nerve Sheath; Malignant Epithelioid Tumor of Peripheral Nerve Sheath; Malignant Epithelioid Peripheral Nerve Sheath Neoplasm; Epithelioid MPNST; Malignant Epithelioid Tumor of the Peripheral Nerve Sheath; Malignant Epithelioid Peripheral Nerve Sheath Tumor;

NCIt definition : A rare variant of malignant peripheral nerve sheath tumor composed predominantly or exclusively of epithelioid cells.;

Neoplastic status : Malignant;

Details

Origin ID

C6561;

UMLS CUI

C1321427;

Automatic exact mappings (from CISMeF team)
- Epithelioid malignant nerve sheath tumor (disorder) [SNOMED CT concept]
- Epithelioid malignant nerve sheath tumor (morphologic abnormality) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumor (morphologic abnormality) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumour, epithelioid [ICD-11 Extension code]
- epithelioid malignant peripheral nerve sheath tumor [DO Concept]
- neurofibrosarcoma [SNOMED Notion]
DO Cross reference
- epithelioid malignant peripheral nerve sheath tumor [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Geographic Necrosis [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Epithelioid malignant nerve sheath tumor (disorder) [SNOMED CT concept]
- Epithelioid malignant nerve sheath tumor (morphologic abnormality) [SNOMED CT concept]
- epithelioid malignant peripheral nerve sheath tumor [DO Concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Hyperchromatic Spindle Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Epithelioid Cell [NCIt concept]
- Malignant Perineural Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Neuroepithelial Cell and Neoplastic Perineural Cell [NCIt concept]
- Neoplastic Perineural Cell [NCIt concept]
disease_has_finding
- Diffuse Pattern [NCIt concept]
- Firm Mass [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Necrotic Change [NCIt concept]
- Pseudoencapsulated Mass [NCIt concept]
disease_has_normal_cell_origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
- Perineural Cell [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Nerve Tissue and Nerve Sheaths [NCIt concept]
- Nerve Tissue, Neuroepithelial Tissue, and Nerve Sheaths [NCIt concept]
disease_has_primary_anatomic_site
- Peripheral Nerve [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Loss of Chromosome 22 [NCIt concept]
disease_may_have_molecular_abnormality
- SMARCB1 Gene Inactivation [NCIt concept]
- TP53 Gene Inactivation [NCIt concept]

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