Preferred Label : Mediastinal Yolk Sac Tumor;
NCIt synonyms : Mediastinal Endodermal Sinus Neoplasm; Endodermal Sinus Neoplasm of Mediastinum; Yolk Sac Neoplasm of Mediastinum; Endodermal Sinus Tumor of the Mediastinum; Yolk Sac Tumor of Mediastinum; Endodermal Sinus Tumor of Mediastinum; Mediastinal Yolk Sac Neoplasm; Endodermal Sinus Neoplasm of the Mediastinum; Yolk Sac Tumor of the Mediastinum; Yolk Sac Neoplasm of the Mediastinum; Mediastinal Endodermal Sinus Tumor;
NCIt definition : An extragonadal non-seminomatous malignant germ cell tumor that arises from the mediastinum.
It is characterized by the presence of small pale cells with small amount of cytoplasm
and round to oval nuclei with small nucleoli forming a variety of patterns, including
microcystic, macrocystic, pseudopapillary, myxomatous, hepatoid, polyvesicular vitelline,
and solid. It manifests with respiratory distress, thoracic pain, fever, and superior
vena cava syndrome.;
Neoplastic status : Malignant;
Origin ID : C6443;
UMLS CUI : C1334683;
- Disease excludes abnormal cell
- Disease may have findings
- Excludes anatomical site(s)
- Has associated anatomic sites
- Semantic type(s)
- disease_excludes_finding
- disease_has_abnormal_cell
- disease_has_finding
- disease_has_normal_cell_origin
- disease_has_normal_tissue_origin
- disease_has_primary_anatomic_site
- disease_may_have_cytogenetic_abnormality