NCIt definition : An X-linked immunodeficiency syndrome that exclusively affects males, although females
can be carriers. It is caused by mutation(s) in SH2D1A and/or XIAP genes and is characterized
by life-threatening episodes of infectious mononucleosis, hypogammaglobulinemia, and
subsequent development of lymphomas (usually B-cell lymphomas) and other lymphoproliferative
disorders.;