Cardiac Epithelioid Hemangioendothelioma

Preferred Label : Cardiac Epithelioid Hemangioendothelioma;

NCIt synonyms : Epithelioid Angioendothelioma of the Heart; Heart Epithelioid Angioendothelioma; Epithelioid Hemangioendothelioma of Heart; Heart Epithelioid Hemangioendothelioma; Cardiac Epithelioid Angioendothelioma; Epithelioid Hemangioendothelioma of the Heart; Epithelioid Angioendothelioma of Heart; Cardiac Hemangioendothelioma;

NCIt definition : A low-grade malignant blood vessel neoplasm, arising from the heart. IIt is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma.;

Neoplastic status : Malignant;

Details

Origin ID

C5362;

UMLS CUI

C1332846;

Disease may have findings
- Painful Mass [NCIt concept]
Excludes anatomical site(s)
- Neck [NCIt concept]
- Pericardial Cavity [NCIt concept]
Has associated anatomic sites
- Cardiovascular System [NCIt concept]
- Heart [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
- Vascular System [NCIt concept]
Has cytogenetic abnormalities
- t(1;3)(p36;q23-25) [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Borderline Lesion [NCIt concept]
- High Grade Lesion [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Endothelial Cell [NCIt concept]
- Malignant Epithelioid Endothelial Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Endothelial Cell [NCIt concept]
disease_has_finding
- Hyalinized Stroma Formation [NCIt concept]
- Low Grade Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Myxoid Stroma Formation [NCIt concept]
- Solitary Mass [NCIt concept]
- Vascular Channel Formation [NCIt concept]
disease_has_normal_cell_origin
- Endothelial Cell [NCIt concept]
disease_has_normal_tissue_origin
- Blood Vessel Endothelium [NCIt concept]
- Vascular Endothelium [NCIt concept]
disease_has_primary_anatomic_site
- Blood Vessel [NCIt concept]
- Heart [NCIt concept]
- Vascular System [NCIt concept]

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