Pleomorphic Hyalinizing Angiectatic Tumor of Soft Parts

Preferred Label : Pleomorphic Hyalinizing Angiectatic Tumor of Soft Parts;

NCIt synonyms : PHAT; Early Pleomorphic Hyalinizing Angiectatic Tumor;

NCIt definition : A non-metastasizing soft tissue neoplasm characterized by the presence of a neoplastic stroma containing spindle cells, dilated thin-walled vessels lined by fibrin, and a chronic inflammatory infiltrate. The majority of cases develop in the subcutaneous tissues usually in the lower extremities and present as slow growing masses. Recurrences occur in approximately half of the cases.;

Neoplastic status : Benign;

Details

Origin ID

C53594;

UMLS CUI

C1709569;

Automatic exact mappings (from CISMeF team)
- Pleomorphic hyalinizing angiectatic tumor of soft tissue (disorder) [SNOMED CT concept]
Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Disease may have findings
- Recurrent Disease [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Pleomorphic hyalinizing angiectatic tumor of soft tissue (disorder) [SNOMED CT concept]
concept_is_in_subset
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Spindle Cell [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Chronic Inflammatory Infiltrate [NCIt concept]
- Dilated Thin-Walled Vascular Space Formation [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Lobulated Growth Pattern [NCIt concept]
- Slow Growing Mass [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_may_have_cytogenetic_abnormality
- OGA (MGEA5) Gene Rearrangement [NCIt concept]
- TGFBR3 Gene Rearrangement [NCIt concept]

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