Myxoinflammatory Fibroblastic Sarcoma

Preferred Label : Myxoinflammatory Fibroblastic Sarcoma;

NCIt synonyms : Inflammatory Myxohyaline Tumor of the Distal Extremities with Virocyte/Reed-Sternberg-Like Cells; Acral Myxoinflammatory Fibroblastic Sarcoma; Inflammatory Myxoid Tumor of the Soft Parts with Bizarre Giant Cells; MIFS;

NCIt related terms : Myxoinflammatory fibroblastic sarcoma (MIFS);

NCIt definition : A low grade, locally aggressive, fibroblastic neoplasm that occurs primarily in the distal extremities. It is characterized by the presence of spindle-shaped fibroblasts, multivacuolated lipoblast-like cells, bizarre ganglion-like cells with inclusion-like nuclei, myxoid stroma formation, and a mixture of acute and chronic inflammatory cells. Distant metastases are very rare.;

Neoplastic status : Malignant;

Details

Origin ID

C49025;

UMLS CUI

C1709103;

Automatic exact mappings (from CISMeF team)
- Myxoinflammatory fibroblastic sarcoma [ICD-11 Extension code]
- Myxoinflammatory fibroblastic sarcoma (morphologic abnormality) [SNOMED CT concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Myxoinflammatory fibroblastic sarcoma (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Ganglion-Like Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Fibroblast [NCIt concept]
- Malignant Spindle-Shaped Fibroblast [NCIt concept]
- Multilobated Lipoblast-Like Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Fibroblast [NCIt concept]
disease_has_finding
- Acute Inflammatory Infiltrate [NCIt concept]
- Chronic Inflammatory Infiltrate [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Inclusion-Like Nucleoli [NCIt concept]
- Low Grade Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Myxoid Stroma Formation [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Fibroblast [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Dermis [NCIt concept]
- Skin [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients