Dedifferentiated Chordoma

Preferred Label : Dedifferentiated Chordoma;

NCIt synonyms : Sarcomatoid Chordoma;

NCIt definition : A high-grade malignant bone tumor arising from the remnants of the notochord. It is characterized by a lobulated growth pattern, myxoid stroma formation, the presence of physaliphorous cells, and a sarcomatous component.;

Neoplastic status : Malignant;

ICD-O code : 9372/3;

Details

Origin ID

C48876;

UMLS CUI

C1266174;

Automatic exact mappings (from CISMeF team)
- Dedifferentiated chordoma [ICD-O code]
- Dedifferentiated chordoma [ICD-11 Extension code]
Disease excludes normal cell origin
- Bone Marrow Stem Cell [NCIt concept]
Has associated anatomic sites
- Bone [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Musculoskeletal System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
disease_excludes_normal_tissue_origin
- Germinal Layer [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Epithelioid Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Physaliphorous Cell [NCIt concept]
disease_has_finding
- High Grade Lesion [NCIt concept]
- Lobulated Growth Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Myxoid Stroma Formation [NCIt concept]
- Sarcomatous Component Present [NCIt concept]
- Slow Growing Mass [NCIt concept]
- Solitary Mass [NCIt concept]
disease_has_normal_cell_origin
- Embryonic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Embryonic Tissue [NCIt concept]
- Remnants of the Notochord [NCIt concept]
disease_has_primary_anatomic_site
- Bone [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Gain of Chromosome 20 [NCIt concept]
- Gain of Chromosome 5q [NCIt concept]
- Gain of Chromosome 7q [NCIt concept]
- Loss of Chromosome 10 [NCIt concept]
- Loss of Chromosome 13 [NCIt concept]
- Loss of Chromosome 3 [NCIt concept]
- Loss of Chromosome 4 [NCIt concept]

Keyword's position in hierarchy(ies) :

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