NCIt definition : An aminothiol salt used in the treatment of nephropathic cystinosis. Cysteamine bitartrate
enters the cell and reacts with cystine producing cysteine and cysteine-cysteamine
mixed disulfide compound, both of which, unlike cystine, can pass through the lysosomal
membrane. This prevents the accumulation of cystine crystals in the lysosomes of patients
with cystinosis, which can cause considerable damage and eventual destruction of the
cells, particularly in the kidneys. (NCI05);