Ectomesenchymoma

Preferred Label : Ectomesenchymoma;

NCIt synonyms : Sarcoma with Ganglionic or Neuroectodermal Differentiation; Malignant Ectomesenchymoma; Rhabdomyosarcoma with Ganglionic Differentiation;

NCIt definition : An exceedingly rare, aggressive malignant mesenchymal neoplasm characterized by the presence of a sarcomatous component and a ganglionic or a neuroectodermal component.;

Alternative definition : NCI-GLOSS: A rare, fast-growing tumor of the nervous system or soft tissue that occurs in children and young adults. Ectomesenchymomas may form in the head and neck, abdomen, perineum, scrotum, or limbs.;

Neoplastic status : Malignant;

ICD-O code : 8921/3;

Codes from synonyms : CDR0000518306; CDR0000539499;

Details

Origin ID

C4716;

UMLS CUI

C0431111;

Automatic exact mappings (from CISMeF team)
- Ectomesenchymoma [ICD-11 Extension code]
- Rhabdomyosarcoma with ganglionic differentiation [ICD-O code]
Currated CISMeF NLP mapping
- Rhabdomyosarcoma with ganglionic differentiation (morphologic abnormality) [SNOMED CT concept]
- ectomesenchymoma [DO Concept]
- ectomesenchymoma [Disease (Nov.)]
DO Cross reference
- ectomesenchymoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Neuroectodermal Differentiation [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Rhabdomyosarcoma with ganglionic differentiation (morphologic abnormality) [SNOMED CT concept]
- ectomesenchymoma [DO Concept]
- ectomesenchymoma [Disease (Nov.)]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- High Grade Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_may_have_abnormal_cell
- Ganglion-Like Cell [NCIt concept]
disease_may_have_molecular_abnormality
- HRAS Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients