Cystic Tumor of the Atrioventricular Node - CISMeF
Cystic Tumor of the Atrioventricular NodeNCIt concept
Preferred Label : Cystic Tumor of the Atrioventricular Node;
NCIt synonyms : Mesothelioma of Atrioventricular Node; Tawarian Node; Intracardiac Endodermal Heterotopia; Endodermal Rest; Benign Mesothelioma of Mahaim; Cystic Tumor of Atrioventricular Node;
NCIt related terms : Cystic tumor of atrio-ventricular node;
NCIt definition : A multicystic tumor arising in the inferior interatrial septum in the region of the
atrioventricular node. The vast majority of patients present with complete heart block
and a minority with partial heart block. Sudden death is reported in approximately
10% of the cases. It is a morphologically benign tumor composed of cuboidal, transitional,
or squamoid cells. The cells may also show sebaceous differentiation and originate
from the endoderm.;