NCIt synonyms : Primary Cutaneous CD4-Positive Small/Medium-Sized Pleomorphic T-Cell Lymphoproliferative
Disorder; Primary Cutaneous CD4-Positive Small Medium-Sized Pleomorphic T-Cell Lymphoma; Primary Cutaneous CD4-Positive Small/Medium-Sized T-Cell Lymphoproliferative Disorder; Primary Cutaneous CD4-Positive Small or Medium T-Cell Lymphoproliferative Disorder;
NCIt related terms : Primary cutaneous CD4-positive small/medium T-cell lymphoma;
NCIt definition : A primary cutaneous T-cell lymphoproliferative disorder. It usually presents with
a solitary plaque or tumor on the face, neck, or upper trunk. Morphologically, it
is composed of small to medium-sized CD4-positive, CD8-negative, and CD30-negative
pleomorphic T-lymphocytes. A small number of large pleomorphic T-lymphocytes may also
be present. The lymphocytic infiltrate is dermal. Focal epidermotropism and subcutaneous
involvement may be present. The clinical behavior is almost always indolent and most
patients present with localized disease.;
Neoplastic status : Uncertain Malignant Potential;