Primary Cutaneous Diffuse Large B-Cell Lymphoma, Leg Type - CISMeF
Primary Cutaneous Diffuse Large B-Cell Lymphoma, Leg TypeNCIt concept
Preferred Label : Primary Cutaneous Diffuse Large B-Cell Lymphoma, Leg Type;
NCIt synonyms : Primary Cutaneous Diffuse Large B-Cell Lymphoma Leg Type; Primary Cutaneous Diffuse Large B-Cell Lymphoma, Leg-Type;
NCIt related terms : Primary cutaneous DLBCL, leg type;
NCIt definition : An aggressive primary cutaneous B-cell lymphoma, usually involving the lower leg.
It is composed of a generally monotonous proliferation of immunoblasts, or less frequently
centroblasts, with few admixed reactive cells. This type of lymphoma occurs most often
in elderly women who present with rapidly growing tumors, usually on one or both legs.
Dissemination to extracutaneous sites is frequent. Treatment with combination chemotherapy
is usually required.;