Intravascular Large B-Cell Lymphoma

Preferred Label : Intravascular Large B-Cell Lymphoma;

NCIt synonyms : Angiotropic Lymphoma; Malignant Angioendotheliomatosis; Angiotropic Large Cell Lymphoma; IVLBCL;

NCIt related terms : Intravascular B-cell lymphoma;

NCIt definition : A rare extranodal B-cell non-Hodgkin lymphoma, characterized by the presence of lymphoma cells exclusively in the lumina of small vessels, particularly capillaries. This is an extremely aggressive lymphoma which responds poorly to chemotherapy. (WHO, 2001);

Neoplastic status : Malignant;

ICD-O code : 9712/3;

Details

Origin ID

C4342;

UMLS CUI

C0334660;

Automatic exact mappings (from CISMeF team)
- Malignant lymphoma, large B-cell, diffuse, no International Classification of Diseases for Oncology subtype (morphologic abnormality) [SNOMED CT concept]
- Other non-follicular lymphoma [ICD-10 Sub-category]
- malignant lymphoma, large cell, diffuse, nos [SNOMED Notion]
Currated CISMeF NLP mapping
- Angioendotheliomatosis (disorder) [SNOMED CT concept]
- Intravascular large B-cell lymphoma [ICD-11 More detail]
- Intravascular large B-cell lymphoma [ICD-11 Subcategory]
- Intravascular large B-cell lymphoma [ICD-O code]
- Intravascular large B-cell lymphoma [ORDO Disease]
- Intravascular large B-cell lymphoma [MedDRA LLT]
- Intravascular large B-cell lymphoma (disorder) [SNOMED CT concept]
- intravascular large B cell lymphoma [Disease (Nov.)]
Disease excludes abnormal cell
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor B-Lymphoblast [NCIt concept]
Disease may have findings
- Hypertension [NCIt concept]
- Leukopenia [NCIt concept]
- Pancytopenia [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Vascular System [NCIt concept]
See also inter- (CISMeF)
- Intravascular large B-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Angioendotheliomatosis (disorder) [SNOMED CT concept]
- Intravascular large B-cell lymphoma [MedDRA LLT]
- Intravascular large B-cell lymphoma [ICD-O code]
- Intravascular large B-cell lymphoma [ORDO Disease]
- Intravascular large B-cell lymphoma (disorder) [SNOMED CT concept]
- Intravascular large B-cell lymphoma (morphologic abnormality) [SNOMED CT concept]
- intravascular large B cell lymphoma [Disease (Nov.)]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Large B-Lymphocyte [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
disease_has_finding
- Diffuse Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Kappa Light Chain Gene Rearrangement [NCIt concept]
disease_has_normal_cell_origin
- B-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Mature B-Lymphocyte [NCIt concept]
- Transformed Peripheral B-Lymphocyte [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
disease_may_have_associated_disease
- Autoimmune Hemolytic Anemia [NCIt concept]
- Dementia [NCIt concept]
- Disseminated Intravascular Coagulation [NCIt concept]
- Nephrotic Syndrome [NCIt concept]
disease_may_have_molecular_abnormality
- Clonal Immunoglobulin Heavy Chain Gene Rearrangement [NCIt concept]
- Clonal Immunoglobulin Lambda Light Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients